FGF10 Signaling differences between type I pleuropulmonary blastoma and congenital cystic adenomatoid malformation
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منابع مشابه
FGF10 Signaling differences between type I pleuropulmonary blastoma and congenital cystic adenomatoid malformation
BACKGROUND Type I pleuropulmonary blastoma (PPB) and congenital cystic adenomatoid malformation of the lung (CCAM) are cystic lung diseases of childhood. Their clinical and radiological presentations are often similar, and pathologic discrimination remains difficult in many cases. As a consequence, type I PPB and CCAM are frequently confused, leading to delayed adequate management for type I PP...
متن کاملCongenital cystic adenomatoid malformation type I
Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway malformation with incidence ranging between 1:10,000 and 1:35,000 newborns. Currently CCAM is classified into five groups according to clinical and pathological features. The clinical outcome varies depending on the subtype and the extent of involvement. The authors report the case of a premature m...
متن کاملCongenital cystic adenomatoid malformation
Australasian Journal of Ultrasound in Medicine August 2009; 12 (3) Introduction Congenital cystic adenomatoid malformation (CCAM) is an uncommon fetal lung anomaly involving cystic changes to the terminal bronchioles. The condition requires close monitoring during the antenatal period with ultrasound in addition to input from the neonatal and paediatric surgical teams. This case study involves ...
متن کاملCongenital Cystic Adenomatoid Malformation (CCAM) with Two Cases Introduction
CCAM is a rare conolition in the neonatal Period. Two babies were admitted to Mofid hospital with cyanosis and respiratory distress. Pneumectomy was done for both of them for space occupaying lesion. Pathology examination of first case showed area of cuboidal epithelium lined tubes and spaces resembling fetal bronchioles, which are torn in folds. In second case, pathologic examination revealed...
متن کامل[Congenital cystic adenomatoid malformation: a case report].
Cystic adenomatoid malformation is a rare pulmonary hamartomatous lesion, of an unknown etiology. Report a singular case of CAM of one newborn, with marked respiratory distress. Using different method (chest X-ray, Multidetector row CT associated at multiplanar and three-dimensional reconstructions), we obtained an accurate diagnosis of site and nature, critical for a correct therapeutic approach.
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ژورنال
عنوان ژورنال: Orphanet Journal of Rare Diseases
سال: 2013
ISSN: 1750-1172
DOI: 10.1186/1750-1172-8-130